Sindrom Rapunzel: Laporan Kasus

https://doi.org/10.35912/jimi.v1i2.730
Published: Apr 12, 2022

Abstract:

Purpose: This study aimed to summarize the general history, physical exam findings, confirmation test, and treatment of a patient with rapunzel syndrome.

Research Methodology: This article is a pediatric surgery RSUD Abdoel Moeloek Lampung case report in 11 March 2020. The subject of the case is a 11-year-old girl who is hospitalized in the hospital ward with Rapunzel syndrome.

Result: A 11-year-old girl, an inpatient in the Pediatric surgery Ward, RSUD Abdoel Moeloek Lampung, with abdominal pain such as squeezing, nausea and vomiting filled with water and hard and little bowel movements.. On physical examination, bloated abdomen, epigastric tenderness and left hypochondrium, mass (+).on ct scan examination with gastric contrast looks enlarged, isodense lesions appear, irregular edges in the gastric lumen to the duodenum, separated from the wall, post contrast does not appear enhanced. The patient was clinically diagnosed with “Rapunzel Syndrome.” Management of the patient during treatment was upper midline laparatomy.

Limitations: This case report is limited to rapunzel syndrome cases with a scarce number of cases and rare cases in children.

Contribution: This case report can be helpful in medical education or used as a reference in making relevant case reports and can be applied in the hospital area when there are cases of Rapunzel syndrome.

Keywords:
1. Rapunzel Synrome
2. Rare Disease
Authors:
1 . Khairun Nisa Berawi
2 . Fauziyyah Nuur Al Azizah
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How to Cite
Berawi, K. N. ., & Al Azizah, F. N. . (2022). Sindrom Rapunzel: Laporan Kasus. Jurnal Ilmu Medis Indonesia, 1(2), 103–112. https://doi.org/10.35912/jimi.v1i2.730
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Issue & Section
Vol. 1 No. 2 (2022): Maret
Articles
References

    Chana, R., & Kumar, R. (2004). Gastrointestinal bezoars in children with special reference to recurrent trichobezoar. Journal of Indian Association of Pediatric Surgeons, 9(1), 25.

    Coulter, R., Antony, M. T., Bhuta, P., & Memon, M. A. (2005). Large gastric trichobezoar in a normal healthy woman: case report and review of pertinent literature. Southern medical journal, 98(10), 1042-1044.

    Dixit, A., Raza, M. A., & Tiwari, R. (2016). Gastric trichobezoar with Rapunzel syndrome: A case report. Journal of Clinical and Diagnostic Research: JCDR, 10(2), PD10.

    Duncan, N. D., Aitken, R., Venugopal, S., West, W., & Carpenter, R. (1994). The Rapunzel syndrome. Report of a case and review of the literature. The West Indian medical journal, 43(2), 63-65.

    Emre, A. U., Tascilar, O., Karadeniz, G., Irkorucu, O., Karakaya, K., & Comert, M. (2008). Rapunzel syndrome of a cotton bezoar in a multimorbid patient. Clinics, 63, 285-288.

    Fernández-López, A.-J., González-Valverde, F. M., & Rodenas-Moncada, J. (2014). Trichophagia and trichobezoar. Cirugía Española, 92(6), 448-449.

    Frey, A. S., McKee, M., King, R. A., & Martin, A. (2005). Hair apparent: Rapunzel syndrome. American Journal of Psychiatry, 162(2), 242-248.

    Gonuguntla, V., & Joshi, D.-D. (2009). Rapunzel syndrome: a comprehensive review of an unusual case of trichobezoar. Clinical medicine & research, 7(3), 99-102.

    Gorter, R., Kneepkens, C., Mattens, E., Aronson, D., & Heij, H. (2010). Management of trichobezoar: case report and literature review. Pediatric surgery international, 26(5), 457-463.

    Hirugade, S., Talpallikar, M., Deshpande, A., Gavali, J., & Borwankar, S. (2001). Rapunzel syndrome with a long tail. The Indian Journal of Pediatrics, 68(9), 895-896.

    Kajal, P., Bhutani, N., Tyagi, N., & Arya, P. (2017). Trichobezoar with and without Rapunzel syndrome in paediatric population: A case series from a tertiary care centre of Northern India. International journal of surgery case reports, 40, 23-26.

    Kesuma, S. K. (2009). Gambaran Tingkat Kecemasan Mahasiswa Kedokteran yang Mengikuti Uji Kompetensi Mahasiswa Program Profesi Dokter di Fakultas Kedokteran Universitas Tanjungpura Tahun 2017. Jurnal Mahasiswa PSPD FK Universitas Tanjungpura, 3(2).

    Mohite, P. N., Gohil, A. B., Wala, H. B., & Vaza, M. A. (2008). Rapunzel syndrome complicated with gastric perforation diagnosed on operation table. Journal of Gastrointestinal Surgery, 12(12), 2240-2242.

    Naik, S., Gupta, V., Naik, S., Rangole, A., Chaudhary, A. K., Jain, P., et al. (2007). Rapunzel syndrome reviewed and redefined. Digestive surgery, 24(3), 157-161.

    Nair, M., & Nair, B. (2008). A rare presentation of Rapunzel syndrome manifesting in the immediate post-appendicectomy period. The Internet Journal of Surgery, 14(2).

    Pace, A. M., & Fearne, C. (2003). Trichobezoar in a 13 year old male: a case report and review of literature.

    Phillips, M. R., Zaheer, S., & Drugas, G. T. (1998). Gastric trichobezoar: case report and literature review. Paper presented at the Mayo Clinic Proceedings.

    Prasad, A., Jain, A., Gupta, A., & Kamra, A. (2018). Trichobezoar: ravenous for hair. Euroasian Journal of Hepato-gastroenterology, 8(1), 97.

    Rabie, M. E., Arishi, A. R., Khan, A., Ageely, H., El-Nasr, G. A. S., & Fagihi, M. (2008). Rapunzel syndrome: the unsuspected culprit. World journal of gastroenterology: WJG, 14(7), 1141.

    Sadock, B. (2015). Kaplan & Sadock’s Comprehrensive Textbook of Psychiatry, 9th edn., Wolster Kluwer: Lippincott Williams and Wilkins, Philadelphia, PA.

    Ullah, W., Saleem, K., Ahmad, E., & Anwer, F. (2016). Rapunzel syndrome: a rare cause of hypoproteinaemia and review of literature. Case Reports, 2016, bcr2016216600.

    Vaughan Jr, E., Sawyers, J., & Scott Jr, H. (1968). The Rapunzel syndrome. An unusual complication of intestinal bezoar. Surgery, 63(2), 339-343.

    Wang, Z., Cao, F., Liu, D., Fang, Y., & Li, F. (2016). The diagnosis and treatment of Rapunzel syndrome. Acta Radiologica Open, 5(11), 2058460115627660.

  1. Chana, R., & Kumar, R. (2004). Gastrointestinal bezoars in children with special reference to recurrent trichobezoar. Journal of Indian Association of Pediatric Surgeons, 9(1), 25.
  2. Coulter, R., Antony, M. T., Bhuta, P., & Memon, M. A. (2005). Large gastric trichobezoar in a normal healthy woman: case report and review of pertinent literature. Southern medical journal, 98(10), 1042-1044.
  3. Dixit, A., Raza, M. A., & Tiwari, R. (2016). Gastric trichobezoar with Rapunzel syndrome: A case report. Journal of Clinical and Diagnostic Research: JCDR, 10(2), PD10.
  4. Duncan, N. D., Aitken, R., Venugopal, S., West, W., & Carpenter, R. (1994). The Rapunzel syndrome. Report of a case and review of the literature. The West Indian medical journal, 43(2), 63-65.
  5. Emre, A. U., Tascilar, O., Karadeniz, G., Irkorucu, O., Karakaya, K., & Comert, M. (2008). Rapunzel syndrome of a cotton bezoar in a multimorbid patient. Clinics, 63, 285-288.
  6. Fernández-López, A.-J., González-Valverde, F. M., & Rodenas-Moncada, J. (2014). Trichophagia and trichobezoar. Cirugía Española, 92(6), 448-449.
  7. Frey, A. S., McKee, M., King, R. A., & Martin, A. (2005). Hair apparent: Rapunzel syndrome. American Journal of Psychiatry, 162(2), 242-248.
  8. Gonuguntla, V., & Joshi, D.-D. (2009). Rapunzel syndrome: a comprehensive review of an unusual case of trichobezoar. Clinical medicine & research, 7(3), 99-102.
  9. Gorter, R., Kneepkens, C., Mattens, E., Aronson, D., & Heij, H. (2010). Management of trichobezoar: case report and literature review. Pediatric surgery international, 26(5), 457-463.
  10. Hirugade, S., Talpallikar, M., Deshpande, A., Gavali, J., & Borwankar, S. (2001). Rapunzel syndrome with a long tail. The Indian Journal of Pediatrics, 68(9), 895-896.
  11. Kajal, P., Bhutani, N., Tyagi, N., & Arya, P. (2017). Trichobezoar with and without Rapunzel syndrome in paediatric population: A case series from a tertiary care centre of Northern India. International journal of surgery case reports, 40, 23-26.
  12. Kesuma, S. K. (2009). Gambaran Tingkat Kecemasan Mahasiswa Kedokteran yang Mengikuti Uji Kompetensi Mahasiswa Program Profesi Dokter di Fakultas Kedokteran Universitas Tanjungpura Tahun 2017. Jurnal Mahasiswa PSPD FK Universitas Tanjungpura, 3(2).
  13. Mohite, P. N., Gohil, A. B., Wala, H. B., & Vaza, M. A. (2008). Rapunzel syndrome complicated with gastric perforation diagnosed on operation table. Journal of Gastrointestinal Surgery, 12(12), 2240-2242.
  14. Naik, S., Gupta, V., Naik, S., Rangole, A., Chaudhary, A. K., Jain, P., et al. (2007). Rapunzel syndrome reviewed and redefined. Digestive surgery, 24(3), 157-161.
  15. Nair, M., & Nair, B. (2008). A rare presentation of Rapunzel syndrome manifesting in the immediate post-appendicectomy period. The Internet Journal of Surgery, 14(2).
  16. Pace, A. M., & Fearne, C. (2003). Trichobezoar in a 13 year old male: a case report and review of literature.
  17. Phillips, M. R., Zaheer, S., & Drugas, G. T. (1998). Gastric trichobezoar: case report and literature review. Paper presented at the Mayo Clinic Proceedings.
  18. Prasad, A., Jain, A., Gupta, A., & Kamra, A. (2018). Trichobezoar: ravenous for hair. Euroasian Journal of Hepato-gastroenterology, 8(1), 97.
  19. Rabie, M. E., Arishi, A. R., Khan, A., Ageely, H., El-Nasr, G. A. S., & Fagihi, M. (2008). Rapunzel syndrome: the unsuspected culprit. World journal of gastroenterology: WJG, 14(7), 1141.
  20. Sadock, B. (2015). Kaplan & Sadock’s Comprehrensive Textbook of Psychiatry, 9th edn., Wolster Kluwer: Lippincott Williams and Wilkins, Philadelphia, PA.
  21. Ullah, W., Saleem, K., Ahmad, E., & Anwer, F. (2016). Rapunzel syndrome: a rare cause of hypoproteinaemia and review of literature. Case Reports, 2016, bcr2016216600.
  22. Vaughan Jr, E., Sawyers, J., & Scott Jr, H. (1968). The Rapunzel syndrome. An unusual complication of intestinal bezoar. Surgery, 63(2), 339-343.
  23. Wang, Z., Cao, F., Liu, D., Fang, Y., & Li, F. (2016). The diagnosis and treatment of Rapunzel syndrome. Acta Radiologica Open, 5(11), 2058460115627660.